Surgical repair of congenital stenosis of the inferior vena cava

The congenital stenosis of the inferior vena cava (IVC) is a rare anomaly causing numerous clinical manifestations, depending on the variant of drainage patterns or collaterals. This case presents a five-year-old Azerbaijani male, who suffered with massive ascites and a leg edema for three months. IVC stenosis was detected on echocardiography, due to a high velocity flow and visualisation of a focal narrowing between the IVC orifice and the proximal end of the hepatic vein entry. The IVC stenosis was confirmed by computed tomography. Surgical dilatation of the IVC using xeno-pericardial patchplasty was performed under the cardiopulmonary bypass. This successful surgical correction of IVC stenosis is the only case ever reported in Azerbaijan.